{"id":1214,"date":"2015-01-16T03:45:33","date_gmt":"2015-01-16T03:45:33","guid":{"rendered":"http:\/\/cardiophile.org\/?p=1214"},"modified":"2023-01-03T09:59:17","modified_gmt":"2023-01-03T04:29:17","slug":"left-ventricular-dysfunction-in-ebsteins-anomaly-of-tricuspid-valve","status":"publish","type":"post","link":"https:\/\/johnsonfrancis.org\/professional\/left-ventricular-dysfunction-in-ebsteins-anomaly-of-tricuspid-valve\/","title":{"rendered":"LV dysfunction in Ebstein&#039;s anomaly"},"content":{"rendered":"<p><iframe loading=\"lazy\" width=\"560\" height=\"315\" src=\"https:\/\/www.youtube.com\/embed\/qBVTM3Wu4dQ\" title=\"YouTube video player\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen=\"\"><\/iframe><\/p>\n<h2><span style=\"color: #008000;\">LV dysfunction in Ebstein&#8217;s anomaly<\/span><\/h2>\n<p>LV dysfunction in Ebstein&#8217;s anomaly: Left ventricular systolic and diastolic dysfunction have been reported in Ebstein&#8217;s anomaly of tricuspid valve, presumably due to the left ventricular fibrosis seen in these cases.<sup>1<\/sup>&nbsp;Left ventricular fibrosis can be due to arterial oxygen desaturation. Left ventricular non compaction is another potential cause of left ventricular dysfunction in cases in which it is associated.<sup>2<\/sup><\/p>\n<p>In a study from Mayo Clinic, <em><strong>50&nbsp;of the 495<\/strong><\/em>&nbsp;patients who underwent surgery for Ebstein&#8217;s anomaly had <strong><em>moderate or severe left ventricular dysfunction<\/em> <\/strong>documented on preoperative echocardiogram.<sup>3&nbsp;<\/sup>Left ventricular function improved in all but four of these patients after surgery. There was no deterioration of left ventricular function after surgery in any of the cases.<\/p>\n<p>Left ventricular diastolic dysfunction in Ebstein&#8217;s anomaly could be due to right ventricular volume overload and it can persist even after intracardiac repair.<sup>4<\/sup><\/p>\n<p><span style=\"color: #0000ff;\"><strong>References<\/strong><\/span><\/p>\n<ol>\n<li>Maruo T, Kano S, Ichino K, Imai Y, Asakawa M, Itoh N, Tamiya E, Ikenouchi H, Hada Y. Ebstein&#8217;s anomaly associated with left ventricular dysfunction: a case report.&nbsp;J Cardiol. 1998;31 Suppl 1:131-6.<\/li>\n<li>Bagur RH, Lederlin M, Montaudon M, Latrabe V, Corneloup O, Iriart X, Laurent F. Images in cardiovascular medicine. Ebstein anomaly associated with left ventricular noncompaction.&nbsp;Circulation. 2008 Oct 14;118(16):e662-4.<\/li>\n<li>Brown ML, Dearani JA, Danielson GK, Cetta F, Connolly HM, Warnes CA, Li Z, Hodge DO, Driscoll DJ.&nbsp;<a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pubmed\/19064031\">Effect of operation for Ebstein anomaly on left ventricular function<\/a>.&nbsp;Am J Cardiol. 2008 Dec 15;102(12):1724-7.<\/li>\n<li>Inai K, Nakanishi T, Mori Y, Tomimatsu H, Nakazawa M.&nbsp;Left ventricular diastolic dysfunction in Ebstein&#8217;s anomaly.&nbsp;Am J Cardiol. 2004 Jan 15;93(2):255-8.<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>LV systolic and diastolic dysfunction have been reported in Ebstein&#8217;s anomaly, presumably due to LV fibrosis due to arterial oxygen desaturation.<\/p>\n","protected":false},"author":1,"featured_media":33463,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"nf_dc_page":"","footnotes":""},"categories":[9],"tags":[],"class_list":["post-1214","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-general"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.9 - 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