{"id":44364,"date":"2021-04-07T14:33:49","date_gmt":"2021-04-07T09:03:49","guid":{"rendered":"https:\/\/johnsonfrancis.org\/professional\/?p=44364"},"modified":"2022-03-03T16:51:15","modified_gmt":"2022-03-03T11:21:15","slug":"takayasu-arteritis","status":"publish","type":"post","link":"https:\/\/johnsonfrancis.org\/professional\/takayasu-arteritis\/","title":{"rendered":"Takayasu arteritis"},"content":{"rendered":"<h2><span style=\"color: #008000;\">Takayasu arteritis<\/span><\/h2>\r\n<p><iframe loading=\"lazy\" title=\"YouTube video player\" src=\"https:\/\/www.youtube.com\/embed\/wv82ZY4YmAg\" width=\"560\" height=\"315\" frameborder=\"0\" allowfullscreen=\"allowfullscreen\"><\/iframe><\/p>\r\n<p>Takayasu arteritis is an inflammatory disorder affecting aorta and its major branches. It is also known as aortoarteritis and pulseless disease [1]. Arteritis leads to thickening of vessel wall, fibrosis, stenosis and thrombus formation. Severe inflammation may weaken the arterial media and lead to aneurysm formation [2].<\/p>\r\n<figure id=\"attachment_53296\" aria-describedby=\"caption-attachment-53296\" style=\"width: 1200px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-53296\" src=\"https:\/\/johnsonfrancis.org\/professional\/wp-content\/uploads\/2014\/09\/Takayasu-arteritis-with-coronary-involvement-Representative-images.jpg\" alt=\"Takayasu arteritis with coronary involvement (Representative images)\" width=\"1200\" height=\"895\" srcset=\"https:\/\/johnsonfrancis.org\/professional\/wp-content\/uploads\/2014\/09\/Takayasu-arteritis-with-coronary-involvement-Representative-images.jpg 1200w, https:\/\/johnsonfrancis.org\/professional\/wp-content\/uploads\/2014\/09\/Takayasu-arteritis-with-coronary-involvement-Representative-images-300x224.jpg 300w, https:\/\/johnsonfrancis.org\/professional\/wp-content\/uploads\/2014\/09\/Takayasu-arteritis-with-coronary-involvement-Representative-images-1024x764.jpg 1024w, https:\/\/johnsonfrancis.org\/professional\/wp-content\/uploads\/2014\/09\/Takayasu-arteritis-with-coronary-involvement-Representative-images-768x573.jpg 768w\" sizes=\"auto, (max-width: 1200px) 100vw, 1200px\" \/><figcaption id=\"caption-attachment-53296\" class=\"wp-caption-text\">Takayasu arteritis with coronary involvement (Representative images)<\/figcaption><\/figure>\r\n<p>Takayasu was an ophthalmologist, who noted characteristic fundal arteriovenous anastomoses in a young female in 1905 and published it in <span class=\"ref-journal\">Acta of the Opthalmic Society of Japan<\/span> in 1908 (<span class=\"ref-vol\">12<\/span>:554\u20135). Onishi and Kagosha described similar cases associated with absent radial pulses in the same year [1].\u00a0<\/p>\r\n<p>A study by Lupi-Herrera E et al reported 107 cases over a 19 year period [3]. In their series, females were predominantly involved (8.5:1). Acute inflammatory phase with systemic and cardiovascular symptoms were noted in half of the cases. 65% had supra aortic trunks and abdominal aortic involvement (Type III in the classification prevalent then). Reduction in amplitude of peripheral pulses was noted in 96%, vascular bruit in 94%, hypertension in 72% and renal artery stenosis in 62%. Heart failure was noted in 28%, but rarely due to coronary arteritis. 48% had previous or current active tuberculosis.<\/p>\r\n<p>Another <a href=\"https:\/\/johnsonfrancis.org\/professional\/natural-history-of-aortoarteritis-takayasus-arteritis\/\">natural history study<\/a> published in 1989 had 88 patients [4]. The cumulative survival of Takayasu arteritis at 5 years was 91% of which event free survival was 74.9%. Ten year survival of Takayasu\u2019s arteritis was 84% of which 64% was event free survival.<\/p>\r\n<p>Ishikawa clinical classification (1978) of Takayasu arteritis had three groups, with two subgroups for group II [5]. Group I had uncomplicated disease, with or without pulmonary artery involvement. Group IIa had mild\/moderate single complications. Group IIb had severe single complication. Group III had two or more complications.<\/p>\r\n<p>An <a href=\"https:\/\/johnsonfrancis.org\/professional\/angiographic-classification-of-takayasu-arteritis\/\">angiographic classification<\/a> was published in 1997, which had types I to V with two subtypes for type II [6]. This was formulated after a retrospective review of 102 Indian and 80 Japanese patients with Takayasu arteritis, comparing their clinical manifestations and angiographic findings.<\/p>\r\n<p><span style=\"color: #0000ff;\"><strong>References<\/strong><\/span><\/p>\r\n<ol>\r\n<li>Johnston SL, Lock RJ, Gompels MM. <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC1769710\/\">Takayasu arteritis: a review<\/a>. J Clin Pathol. 2002 Jul;55(7):481-6.\u00a0<\/li>\r\n<li>Numano F, Okawara M, Inomata H, Kobayashi Y. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/11041416\/\">Takayasu&#8217;s arteritis<\/a>. Lancet. 2000 Sep 16;356(9234):1023-5.<\/li>\r\n<li>Lupi-Herrera E, S\u00e1nchez-Torres G, Marcushamer J, Mispireta J, Horwitz S, Vela JE. Takayasu&#8217;s arteritis. Clinical study of 107 cases. Am Heart J. 1977 Jan;93(1):94-103.\u00a0<\/li>\r\n<li>R Subramanyan, J Joy, K G Balakrishnan. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/2569946\/\">Natural History of Aortoarteritis (Takayasu\u2019s Disease)<\/a>. Circulation. 1989 Sep;80(3):429-37.<\/li>\r\n<li>Ishikawa K. <a href=\"https:\/\/www.ahajournals.org\/doi\/pdf\/10.1161\/01.CIR.57.1.27\">Natural history and classification of occlusive thromboaortopathy (Takayasu&#8217;s disease)<\/a>. Circulation. 1978 Jan;57(1):27-35.\u00a0<\/li>\r\n<li>\r\n<div class=\"citation-text\">Moriwaki R, Noda M, Yajima M, Sharma BK, Numano F. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/9158381\/\">Clinical manifestations of Takayasu arteritis in India and Japan&#8211;new classification of angiographic findings<\/a>. Angiology. 1997 May;48(5):369-79.\u00a0<\/div>\r\n<\/li>\r\n<\/ol>\r\n\r\n<p class=\"wp-block-paragraph\">&nbsp;<\/p>\r\n","protected":false},"excerpt":{"rendered":"<p>Takayasu arteritis Takayasu arteritis is an inflammatory disorder affecting aorta and its major branches. It is also known as aortoarteritis and pulseless disease [1]. Arteritis leads to thickening of vessel wall, fibrosis, stenosis and thrombus formation. Severe inflammation may weaken the arterial media and lead to aneurysm formation [2]. Takayasu was an ophthalmologist, who noted [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":44366,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"nf_dc_page":"","footnotes":""},"categories":[2],"tags":[],"class_list":["post-44364","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-cardiology"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.9 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Takayasu arteritis - All About Cardiovascular System and Disorders<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/johnsonfrancis.org\/professional\/takayasu-arteritis\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Takayasu arteritis - All About Cardiovascular System and Disorders\" \/>\n<meta property=\"og:description\" content=\"Takayasu arteritis Takayasu arteritis is an inflammatory disorder affecting aorta and its major branches. It is also known as aortoarteritis and pulseless disease [1]. Arteritis leads to thickening of vessel wall, fibrosis, stenosis and thrombus formation. Severe inflammation may weaken the arterial media and lead to aneurysm formation [2]. 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