Classification of congenital cyanotic heart diseases

Classification of congenital cyanotic heart diseases

Congenital cyanotic heart diseases can be classified into those with decreased pulmonary blood flow and those with increased pulmonary blood flow. Congenital cyanotic heart diseases with high pulmonary blood flow include transposition of great arteries, double outlet right ventricle, univentricular heart and total anomalous pulmonary venous drainage. Congenital cyanotic heart diseases with low pulmonary blood flow include tetralogy of Fallot, Ebstein’s anomaly of the tricuspid valve, tricuspid atresia and pulmonary atresia. Transposition of great arteries and double outlet right ventricle if associated with severe pulmonary stenosis, can present with reduced pulmonary blood flow, the so called tetralogy of Fallot equivalents.