Clinical signs of pulmonary hypertension are remarkable in Eisenmenger syndrome: left parasternal right ventricular heave, palpable second heart sound.
Hypoplastic left heart syndrome: hypoplasia of left heart at multiple levels - hypoplastic left ventricle, aortic atresia and a hypoplastic ascending aorta.
Evaluation of a patient with grown up congenital heart disease (GUCH) is similar to any other patient and begins with a good history to assess symptoms.