Left atrial myxoma – echocardiogram in parasternal long axis view
Brief Review with Echocardiogram video
Left atrial myxoma in parasternal long axis viewMyxoma is a primary cardiac tumour, which is much less common than the secondary cardiac tumours. Echocardiogram demonstrates left atrial myxoma very well.
Myxoma is seen on echocardiogram in parasternal long axis view as a mass prolapsing into the left ventricle in diastole. The site of attachment of the myxoma is not evident in this view. A four chamber view had shown that it is actually attached to the interatrial septum. Myxoma is the commonest primary cardiac tumour in the adult, and it is usually seen in the left atrium. Right atrial myxomas are rare. Percutaneous ablation and retrieval of a right atrial myxoma has been reported, though usual approach for removal of myxomas is open surgery . Rarely myxomas can occur in the right ventricle  and the left ventricle . Sometimes myxomas can be familial. Familial myxomas can occur as part of Carney’s complex, with associated skin pigmentation abnormalities (lentigines), endocrine tumours and schwannomas . Two thirds of the myxomas associated with Carney’s complex have been shown to have PRKAR1A mutations .
Mosaic mitral regurgitation jet is seen in the left atrium skirting the myxoma anteriorly and left atrial wall posteriorly.
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